I27.0 Primary pulmonary hypertension

Type 1 Excludes:
  • Persistent Pulmonary Hypertension Of Newborn (P29.30)
  • Pulmonary Hypertension NOS (I27.20)
  • Secondary Pulmonary Arterial Hypertension (I27.21)
  • Secondary Pulmonary Hypertension (I27.29)
Applicable To:
  • Heritable Pulmonary Arterial Hypertension
  • Idiopathic Pulmonary Arterial Hypertension
  • Primary Group 1 Pulmonary Hypertension
  • Primary Pulmonary Arterial Hypertension

The following code(s) above I27.0 may contain annotation back-references that may be applicable to I27.0:

Diagnosis Index